Congenital absence of the pulmonary valve

Congenital Absence of the Pulmonary Valve

The autopsy on a 32-year-old man revealed an absence of the pulmonary valve, a ventricular septal defect, and a single coronary artery. Congenital absence of the pulmonary valve has not been previously reported. The diagnosis of the accompanying pulmonary incompetence is discussed in the light of the catheterization studies and clinical findings. The pathologic abnormalities as found at postmor...

Congenital absence of the pulmonary valve

Congenital absence of pulmonary valve leaflets.

Congenital absence of pulmonary valve leaflets is an uncommon condition usually associated with ventricular septal defect and an obstructive pulmonary valve ring. Twenty-one patients with these malformations are described. Twenty had an associated ventricular septal defect with ventriculoarterial concordance, and one also had transposition of the great arteries, ventricular septal defect, and o...

Echocardiographic findings of congenital absence of the pulmonary valve with tetralogy of Fallot.

The characteristic echocardiographic findings for congenital absence of the pulmonary valve with tetralogy of Fallot were described in three patients, whose diagnoses were confirmed by operation and/or autopsy. The abnormal linear echo, which was thought to be derived from the rudimentary pulmonary valve tissue, was recorded anteriorly to the dense echo from the subpulmonary muscle mass. The ec...

Congenital absence of the pulmonary valve associated with tricuspid atresia and intact ventricular septum.

visualized. The left circumflex coronary artery showed an area of 50 percent narrowing prior to its bifurcation into the obtuse marginal branch. In addition, there was a significant 70-80 percent stenosis at the origin of the obtuse marginal branch, with no distal circumflex coronary artery visualized. The right coronary artery was a large vessel and was totally occluded at the acute margin, wi...